Indian Journal of Endocrine Surgery and Research

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VOLUME 16 , ISSUE 1 ( Jan-Jun, 2021 ) > List of Articles


Collagenous Fibroma Mimicking a Retrosternal Goiter: A Case Report

Varghese Thomas, Anish J Cherian, Paul M Jacob

Keywords : Collagenous fibroma, Desmoplastic fibroblastoma, Retrosternal goiter, Soft tissue tumor

Citation Information : Thomas V, Cherian AJ, Jacob PM. Collagenous Fibroma Mimicking a Retrosternal Goiter: A Case Report. 2021; 16 (1):32-34.

DOI: 10.5005/jp-journals-10088-11152

License: CC BY-NC 4.0

Published Online: 26-08-2021

Copyright Statement:  Copyright © 2021; The Author(s).


Collagenous fibroma, earlier known as desmoplastic fibroblastoma, is a rare fibrous soft tissue tumor that has been described more often in the extremities, where it presents as a slow-growing and painless mass. We report a case of a 48-year-old gentleman, who presented with an anterior neck swelling with substernal extension, resembling a retrosternal goiter, after clinical examination and radiological and cytological assessments. Intraoperatively, we found it to be a mass abutting but separate from the thyroid, arising from the deep aspect of sternum inaccessible from the neck requiring partial-sternotomy for excision. Histopathological examination revealed a hypocellular tumor made of spindle to stellate cells with surrounding stroma showing collagenization with collagen bundles to myxoid changes. This report documents a rare differential for goiter, only the second case reported in the central neck.

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