Indian Journal of Endocrine Surgery and Research

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VOLUME 16 , ISSUE 1 ( Jan-Jun, 2021 ) > List of Articles

CASE REPORT

Carney\'s Triad—The Full Syndrome with Four Components: A Case Report

Shreya Surendra, Varghese Thomas, Supriya Sen, Shawn S Thomas, Anish J Cherian, Deepak Thomas Abraham, MJ Paul

Keywords : Carney\'s triad—GIST, Paraganglioma, Pulmonary chondroma

Citation Information : Surendra S, Thomas V, Sen S, Thomas SS, Cherian AJ, Abraham DT, Paul M. Carney\'s Triad—The Full Syndrome with Four Components: A Case Report. 2021; 16 (1):25-27.

DOI: 10.5005/jp-journals-10088-11150

License: CC BY-NC 4.0

Published Online: 26-08-2021

Copyright Statement:  Copyright © 2021; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Carney\'s triad is a rare nonhereditary condition affecting young females. Its prevalence is less than one in a million population.1 It is characterized by gastrointestinal stromal tumors (GISTs), pulmonary chondroma, and extra-adrenal paraganglioma. The genetic alterations in this triad are yet to be understood. It is more appropriately classified as a novel multiple endocrine neoplasia. We report an interesting case of a young lady incidentally detected with tumors composing the triad.


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